Steroid-responsive Encephalopathy Associated with Autoimmune Thyroiditis (SREAT) Presenting with Pure Cerebellar Ataxia

Steroid-responsive Encephalopathy Associated with Autoimmune Thyroiditis (SREAT) Presenting with Pure Cerebellar Ataxia

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Background: Myoclonus and tremor are common movement disorder phenomenologies in steroid-responsive encephalopathy associated with autoimmune thyroiditis (SREAT).Pure ataxia without encephalopathy has rarely been reported.Case report: We report 21- and 40-year-old females who presented with subacute pure ataxia without encephalopathy.After immunotherapies, both exhibited initial improvement of shiro neon zero ataxia, and subsequently remained in plateau phase.Discussion: This treatable velgen vff 12 disorder should be added to the differential diagnoses of progressive cerebellar ataxia, and anti-thyroid peroxidase and anti-thyroglobulin should be considered as part of the workup.

It is crucial not to misdiagnose SREAT presenting with pure cerebellar ataxia as degenerative or spinocerebellar ataxia.